Acute hepatic porphyrias: Recommendations for evaluation and long-term management

Keyphrases

• Long-term Management 100%
• Acute Hepatic Porphyria 100%
• Porphyrin Precursors 50%
• Biochemical Tests 50%
• Newly Diagnosed Patients 25%
• National Institutes of Health 25%
• Clinical Features 25%
• Life-threatening 25%
• Medical Conditions 25%
• Clinical Management 25%
• Clinical Practice Guidelines 25%
• Clinical Trials Network 25%
• Medical History 25%
• Clinical Experience 25%
• Acute Attack 25%
• Porphyria 25%
• Long-term Complications 25%
• Response to Treatment 25%
• Disease Response 25%
• Inherited Disorders 25%
• Specific Enzymes 25%
• Close Monitoring 25%
• Precipitating Factors 25%
• Symptomatic Patients 25%
• Clinical Complications 25%
• Genetic Testing 25%
• Heme Biosynthesis Pathway 25%
• Comprehensive Care 25%
• Subspecialists 25%
• Hepatology 25%
• Natural History Study 25%
• Rare Diseases 25%
• Recurrent Attacks 25%
• Clinical Heterogeneity 25%
• Monitoring Patients 25%
• Clinical Potential 25%
• Monitoring Disease Progression 25%
• Clinical Cohort 25%
• Treatment Modification 25%
• Expert Center 25%
• Diagnostic Confirmation 25%
• Biochemical Monitoring 25%
• Suboptimal Management 25%

Medicine and Dentistry

• Hepatic Porphyria 100%
• Disease 75%
• Porphyrin 50%
• Precursor 50%
• Patient Monitoring 50%
• Diagnosis 25%
• Cohort Effect 25%
• Clinical Research 25%
• Clinical Feature 25%
• Heme 25%
• Clinical Management 25%
• Patient Referral 25%
• Medical History 25%
• Genetic Screening 25%
• Porphyria 25%
• Disease Exacerbation 25%
• Biosynthesis 25%
• Physical Examination 25%
• Clinical Guideline 25%
• Rare Disease 25%
• Hepatology 25%
• Evaluation and Follow up 25%