Bilateral Forearm Pseudotumors in an Adult with Hemophilia A and Ollier Disease: A Case Report

Barkha Gurbani, Matthew Igbinigie, Aristides Koutrouvelis, Jack B. Alperin, Ronald Lindsey

Research output: Contribution to journalArticle

Abstract

CASE: A 29-year-old man with mild hemophilia A and Ollier disease presented with bilateral atraumatic forearm pseudotumors. Both forearm pseudotumors were successfully treated surgically with staged radical extirpation and factor VIII replacement therapy. CONCLUSION: Pseudotumors typically occur in adolescents with severe, poorly controlled hemophilia A. The development of factor VIII replacement therapy has progressively reduced the incidence of pseudotumors in patients in the developed world. No standardized therapy exists for pseudotumors that continue to bleed into the muscles despite nonoperative measures. Persistent masses require surgical removal with careful preoperative planning and a team approach.

Original languageEnglish (US)
Pages (from-to)e54
JournalJBJS case connector
Volume8
Issue number3
DOIs
StatePublished - Jul 1 2018

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Enchondromatosis
Hemophilia A
Forearm
Factor VIII
N,N-dimethyl-3,3-diphenyl-1-methylallylamine
Therapeutics
Muscles
Incidence

ASJC Scopus subject areas

  • Surgery
  • Orthopedics and Sports Medicine

Cite this

Bilateral Forearm Pseudotumors in an Adult with Hemophilia A and Ollier Disease : A Case Report. / Gurbani, Barkha; Igbinigie, Matthew; Koutrouvelis, Aristides; Alperin, Jack B.; Lindsey, Ronald.

In: JBJS case connector, Vol. 8, No. 3, 01.07.2018, p. e54.

Research output: Contribution to journalArticle

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