Abstract
Parkes Weber syndrome (PWS) is a congenital overgrowth disorder characterized by unilateral limb and axial hypertrophy, capillary malformations of the skin, and high-fow arteriovenous fstulas (AVFs). Spinal AVFs in the setting of PWS are challenging vascular lesions that often contain multiple arteriovenous (AV) shunts. The present case report highlights an adolescent girl with PWS who presented with a ruptured complex high-fow conus medullaris AVF. She was successfully treated with endovascular embolization and microsurgery. At the 2-year follow-up, the patient remained free of neurological symptoms and had no recurrence of the vascular malformation.
Original language | English (US) |
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Pages (from-to) | 234-238 |
Number of pages | 5 |
Journal | Journal of Neurosurgery: Spine |
Volume | 25 |
Issue number | 2 |
DOIs | |
State | Published - Aug 2016 |
Externally published | Yes |
Keywords
- Arteriovenous fistula
- Endovascular
- Parkes Weber syndrome
- Spinal cord
- Treatment
- Vascular disorders
- Vascular malformation
ASJC Scopus subject areas
- Surgery
- Neurology
- Clinical Neurology