Combined surgical and endovascular treatment of complex high-flow conus medullaris arteriovenous fistula associated with Parkes Weber syndrome

Case report

Arya Bagherpour, Gustavo J. Rodriguez, Chetan Moorthy, Todd T. Trier, Alberto Maud

Research output: Contribution to journalArticle

3 Citations (Scopus)

Abstract

Parkes Weber syndrome (PWS) is a congenital overgrowth disorder characterized by unilateral limb and axial hypertrophy, capillary malformations of the skin, and high-fow arteriovenous fstulas (AVFs). Spinal AVFs in the setting of PWS are challenging vascular lesions that often contain multiple arteriovenous (AV) shunts. The present case report highlights an adolescent girl with PWS who presented with a ruptured complex high-fow conus medullaris AVF. She was successfully treated with endovascular embolization and microsurgery. At the 2-year follow-up, the patient remained free of neurological symptoms and had no recurrence of the vascular malformation.

Original languageEnglish (US)
Pages (from-to)234-238
Number of pages5
JournalJournal of Neurosurgery: Spine
Volume25
Issue number2
DOIs
StatePublished - Aug 1 2016
Externally publishedYes

Fingerprint

Sturge-Weber Syndrome
Arteriovenous Fistula
Spinal Cord
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Vascular Malformations
Microsurgery
Hypertrophy
Blood Vessels
Therapeutics
Extremities
Recurrence
Skin

Keywords

  • Arteriovenous fistula
  • Endovascular
  • Parkes Weber syndrome
  • Spinal cord
  • Treatment
  • Vascular disorders
  • Vascular malformation

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Combined surgical and endovascular treatment of complex high-flow conus medullaris arteriovenous fistula associated with Parkes Weber syndrome : Case report. / Bagherpour, Arya; Rodriguez, Gustavo J.; Moorthy, Chetan; Trier, Todd T.; Maud, Alberto.

In: Journal of Neurosurgery: Spine, Vol. 25, No. 2, 01.08.2016, p. 234-238.

Research output: Contribution to journalArticle

@article{df0ed95fc2364c7dbeda72ee6a52234c,
title = "Combined surgical and endovascular treatment of complex high-flow conus medullaris arteriovenous fistula associated with Parkes Weber syndrome: Case report",
abstract = "Parkes Weber syndrome (PWS) is a congenital overgrowth disorder characterized by unilateral limb and axial hypertrophy, capillary malformations of the skin, and high-fow arteriovenous fstulas (AVFs). Spinal AVFs in the setting of PWS are challenging vascular lesions that often contain multiple arteriovenous (AV) shunts. The present case report highlights an adolescent girl with PWS who presented with a ruptured complex high-fow conus medullaris AVF. She was successfully treated with endovascular embolization and microsurgery. At the 2-year follow-up, the patient remained free of neurological symptoms and had no recurrence of the vascular malformation.",
keywords = "Arteriovenous fistula, Endovascular, Parkes Weber syndrome, Spinal cord, Treatment, Vascular disorders, Vascular malformation",
author = "Arya Bagherpour and Rodriguez, {Gustavo J.} and Chetan Moorthy and Trier, {Todd T.} and Alberto Maud",
year = "2016",
month = "8",
day = "1",
doi = "10.3171/2016.1.SPINE151156",
language = "English (US)",
volume = "25",
pages = "234--238",
journal = "Journal of Neurosurgery: Spine",
issn = "1547-5654",
publisher = "American Association of Neurological Surgeons",
number = "2",

}

TY - JOUR

T1 - Combined surgical and endovascular treatment of complex high-flow conus medullaris arteriovenous fistula associated with Parkes Weber syndrome

T2 - Case report

AU - Bagherpour, Arya

AU - Rodriguez, Gustavo J.

AU - Moorthy, Chetan

AU - Trier, Todd T.

AU - Maud, Alberto

PY - 2016/8/1

Y1 - 2016/8/1

N2 - Parkes Weber syndrome (PWS) is a congenital overgrowth disorder characterized by unilateral limb and axial hypertrophy, capillary malformations of the skin, and high-fow arteriovenous fstulas (AVFs). Spinal AVFs in the setting of PWS are challenging vascular lesions that often contain multiple arteriovenous (AV) shunts. The present case report highlights an adolescent girl with PWS who presented with a ruptured complex high-fow conus medullaris AVF. She was successfully treated with endovascular embolization and microsurgery. At the 2-year follow-up, the patient remained free of neurological symptoms and had no recurrence of the vascular malformation.

AB - Parkes Weber syndrome (PWS) is a congenital overgrowth disorder characterized by unilateral limb and axial hypertrophy, capillary malformations of the skin, and high-fow arteriovenous fstulas (AVFs). Spinal AVFs in the setting of PWS are challenging vascular lesions that often contain multiple arteriovenous (AV) shunts. The present case report highlights an adolescent girl with PWS who presented with a ruptured complex high-fow conus medullaris AVF. She was successfully treated with endovascular embolization and microsurgery. At the 2-year follow-up, the patient remained free of neurological symptoms and had no recurrence of the vascular malformation.

KW - Arteriovenous fistula

KW - Endovascular

KW - Parkes Weber syndrome

KW - Spinal cord

KW - Treatment

KW - Vascular disorders

KW - Vascular malformation

UR - http://www.scopus.com/inward/record.url?scp=84982126531&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=84982126531&partnerID=8YFLogxK

U2 - 10.3171/2016.1.SPINE151156

DO - 10.3171/2016.1.SPINE151156

M3 - Article

VL - 25

SP - 234

EP - 238

JO - Journal of Neurosurgery: Spine

JF - Journal of Neurosurgery: Spine

SN - 1547-5654

IS - 2

ER -