Congenital smooth muscle hamartoma presenting as a linear atrophic plaque: Case report and review of the literature

M. Grau-Massanes, Sharon Raimer, M. Colome-Grimmer, A. Yen, R. L. Sanchez

Research output: Contribution to journalArticle

22 Citations (Scopus)

Abstract

Congenital smooth muscle hamartoma usually manifests as a well- circumscribed, hyperpigmented plaque, frequently hypertrichotic, on the trunk or extremities. We report such a lesion in a 7-month-old girl that presented as a linear, mottled, purplish red plaque appearing in areas to be atrophic, involving her right buttock, posterior thigh and leg, and fifth toe. Although the clinical appearance suggested linear morphea, a biopsy specimen had numerous haphazardly oriented bundles of smooth muscle in the reticular dermis. Masson trichrome staining, smooth muscle specific actin, and electron microscopic studies confirmed the smooth muscle nature of the cells. A diagnosis of smooth muscle hamartoma was made. To our knowledge, this linear clinical presentation has not been described previously.

Original languageEnglish (US)
Pages (from-to)222-225
Number of pages4
JournalPediatric Dermatology
Volume13
Issue number3
StatePublished - May 1996

Fingerprint

Hamartoma
Smooth Muscle
Localized Scleroderma
Buttocks
Toes
Dermis
Thigh
Smooth Muscle Myocytes
Actins
Leg
Extremities
Electrons
Staining and Labeling
Biopsy

ASJC Scopus subject areas

  • Dermatology
  • Pediatrics, Perinatology, and Child Health

Cite this

Grau-Massanes, M., Raimer, S., Colome-Grimmer, M., Yen, A., & Sanchez, R. L. (1996). Congenital smooth muscle hamartoma presenting as a linear atrophic plaque: Case report and review of the literature. Pediatric Dermatology, 13(3), 222-225.

Congenital smooth muscle hamartoma presenting as a linear atrophic plaque : Case report and review of the literature. / Grau-Massanes, M.; Raimer, Sharon; Colome-Grimmer, M.; Yen, A.; Sanchez, R. L.

In: Pediatric Dermatology, Vol. 13, No. 3, 05.1996, p. 222-225.

Research output: Contribution to journalArticle

Grau-Massanes, M, Raimer, S, Colome-Grimmer, M, Yen, A & Sanchez, RL 1996, 'Congenital smooth muscle hamartoma presenting as a linear atrophic plaque: Case report and review of the literature', Pediatric Dermatology, vol. 13, no. 3, pp. 222-225.
Grau-Massanes M, Raimer S, Colome-Grimmer M, Yen A, Sanchez RL. Congenital smooth muscle hamartoma presenting as a linear atrophic plaque: Case report and review of the literature. Pediatric Dermatology. 1996 May;13(3):222-225.
Grau-Massanes, M. ; Raimer, Sharon ; Colome-Grimmer, M. ; Yen, A. ; Sanchez, R. L. / Congenital smooth muscle hamartoma presenting as a linear atrophic plaque : Case report and review of the literature. In: Pediatric Dermatology. 1996 ; Vol. 13, No. 3. pp. 222-225.
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