Double dermal sinus tracts of the cervical and thoracic regions

a case in a 3-year-old child and review of the literature

Oliver D. Mrowczynski, Jessica R. Lane, Mohammadali Mohajel Shoja, Charles S. Specht, Sara T. Langan, Elias B. Rizk

Research output: Contribution to journalArticle

Abstract

Introduction: Dermal sinus tracts are rare congenital abnormalities characterized by an epithelium-lined tract that extends from the subcutaneous tissue to the underlying thecal sac or neural tube. These developmental anomalies can present asymptomatically with a cutaneous dimple or with devastating complications including recurrent episodes of meningitis, or neurological complications including paralysis. Dermal sinus tracts generally occur as single lesions, and the presentation of midline double dermal sinus tracts of the cervical and thoracic regions has not been previously described. Methods: Here, we present the case of a 3-year-old girl suffering from recurrent episodes of myelitis, paraparesis, and intramedullary intradural masses, who was diagnosed with double dermal sinus tracts of the cervical and thoracic regions. We also present a summary of all previous reported cases of multiple dermal sinus tracts. Results: Our patient was successfully treated surgically and is now 2 years status post her last procedure with a significant improvement in her neurologic function and normal muscle strength and tone for her age, and there was no recurrence of her symptoms. Conclusions: Early treatment with prophylactic surgery should be performed when possible, but removal of these lesions once symptoms have arisen can also lead to success, as in the case presented here. Complete excision and intradural exploration is required to excise the complete tract.

Original languageEnglish (US)
Pages (from-to)987-990
Number of pages4
JournalChild's Nervous System
Volume34
Issue number5
DOIs
StatePublished - May 1 2018

Fingerprint

Spina Bifida Occulta
Thorax
Myelitis
Paraparesis
Neural Tube
Subcutaneous Tissue
Muscle Strength
Meningitis
Paralysis
Nervous System
Epithelium
Recurrence
Skin

Keywords

  • Cyst
  • Dermal sinus tract
  • Dermoid
  • Spinal dysraphism

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Clinical Neurology

Cite this

Mrowczynski, O. D., Lane, J. R., Mohajel Shoja, M., Specht, C. S., Langan, S. T., & Rizk, E. B. (2018). Double dermal sinus tracts of the cervical and thoracic regions: a case in a 3-year-old child and review of the literature. Child's Nervous System, 34(5), 987-990. https://doi.org/10.1007/s00381-017-3707-4

Double dermal sinus tracts of the cervical and thoracic regions : a case in a 3-year-old child and review of the literature. / Mrowczynski, Oliver D.; Lane, Jessica R.; Mohajel Shoja, Mohammadali; Specht, Charles S.; Langan, Sara T.; Rizk, Elias B.

In: Child's Nervous System, Vol. 34, No. 5, 01.05.2018, p. 987-990.

Research output: Contribution to journalArticle

Mrowczynski, Oliver D. ; Lane, Jessica R. ; Mohajel Shoja, Mohammadali ; Specht, Charles S. ; Langan, Sara T. ; Rizk, Elias B. / Double dermal sinus tracts of the cervical and thoracic regions : a case in a 3-year-old child and review of the literature. In: Child's Nervous System. 2018 ; Vol. 34, No. 5. pp. 987-990.
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