HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases

Ali Morshid, Amin Moshksar, Aparna Das, Alexander G. Duarte, Diana Palacio, Javier Villanueva-Meyer

Research output: Contribution to journalArticlepeer-review

Abstract

Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia that is often underdiagnosed on computed tomography scans. The disease process involves a combination of fibrosis involving the visceral pleura and fibroelastic changes within the subpleural lung parenchyma. Although definitive diagnosis is based on pathological evaluation, this is often not feasible and pattern recognition on CT as "definite PPFE" or "consistent with PPFE" is important given that sub group of patients will undergo rapid progression with clinical deterioration.

Original languageEnglish (US)
Pages (from-to)1564-1569
Number of pages6
JournalRadiology Case Reports
Volume16
Issue number6
DOIs
StatePublished - Jun 2021

Keywords

  • Chest radiology
  • Idiopathic interstitial pneumonia
  • Pleuro parenchymal fibroelastosis

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging

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