TY - JOUR
T1 - HRCT Diagnosis of Pleuroparenchymal fibroelastosis
T2 - Report of two cases
AU - Morshid, Ali
AU - Moshksar, Amin
AU - Das, Aparna
AU - Duarte, Alexander G.
AU - Palacio, Diana
AU - Villanueva-Meyer, Javier
N1 - Publisher Copyright:
© 2021
PY - 2021/6
Y1 - 2021/6
N2 - Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia that is often underdiagnosed on computed tomography scans. The disease process involves a combination of fibrosis involving the visceral pleura and fibroelastic changes within the subpleural lung parenchyma. Although definitive diagnosis is based on pathological evaluation, this is often not feasible and pattern recognition on CT as "definite PPFE" or "consistent with PPFE" is important given that sub group of patients will undergo rapid progression with clinical deterioration.
AB - Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia that is often underdiagnosed on computed tomography scans. The disease process involves a combination of fibrosis involving the visceral pleura and fibroelastic changes within the subpleural lung parenchyma. Although definitive diagnosis is based on pathological evaluation, this is often not feasible and pattern recognition on CT as "definite PPFE" or "consistent with PPFE" is important given that sub group of patients will undergo rapid progression with clinical deterioration.
KW - Chest radiology
KW - Idiopathic interstitial pneumonia
KW - Pleuro parenchymal fibroelastosis
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U2 - 10.1016/j.radcr.2021.03.051
DO - 10.1016/j.radcr.2021.03.051
M3 - Article
AN - SCOPUS:85104416808
SN - 1930-0433
VL - 16
SP - 1564
EP - 1569
JO - Radiology Case Reports
JF - Radiology Case Reports
IS - 6
ER -