Isolated Frontosphenoidal Suture Craniosynostosis: Treatment Approaches and Literature Review for a Unique Condition

Jordi Puente-Espel, Steven D. Kozusko, Petros Konofaos, Frederick A. Boop, Robert D. Wallace

Research output: Contribution to journalArticlepeer-review

4 Scopus citations

Abstract

Background:Craniosynostosis isolated to the frontosphenoidal suture is an extremely rare entity, distinct from other types of synostotic anterior plagiocephaly, from the embryologic, phenotypic and endocranial morphology viewpoints. Embryologically, the sphenoid bone has two origins, which morphogenetically represent 2 distinct subunits. Depending on the region involved, unique craniofacial features involving the forehead, temporal region and orbit will be demonstrated. A case of frontosphenoidal suture synostosis depicting these features is presented. In addition, a literature review was performed and a treatment algorithm is proposed.

Original languageEnglish (US)
Pages (from-to)E385-E388
JournalJournal of Craniofacial Surgery
Volume31
Issue number4
DOIs
StatePublished - Jun 1 2020
Externally publishedYes

Keywords

  • Craniosynostosis
  • fronto-orbital advancement
  • frontosphenoidal suture
  • harlequin deformity
  • plagiocephaly

ASJC Scopus subject areas

  • Surgery
  • Otorhinolaryngology

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