Kaposiform hemangioendothelioma (with Kasabach Merritt syndrome) of the head and neck

Case report and review of the literature

Shraddha S. Mukerji, Alex J. Osborn, Jess Roberts, Tulio A. Valdez

Research output: Contribution to journalArticle

15 Citations (Scopus)

Abstract

An infant initially diagnosed with a parotid hemangioma presented with stridor and thrombocytopenia. Diagnosis of Kaposiform hemangioendiothelioma was confirmed with biopsy. The child succumbed to multi-system organ failure related to consumptive coagulopathy despite aggressive medical management. Kaposiform hemangioendiothelioma is a rare head and neck tumor that may be mistaken for a hemangioma on preliminary diagnosis, which may lead to increased morbidity and mortality especially in the setting of Kasabach-Merritt phenomenon. A platelet count may provide an early and important clue to the possibility of coagulopathy; prompting physicians to look for a diagnosis other than a simple hemangioma.

Original languageEnglish (US)
Pages (from-to)1474-1476
Number of pages3
JournalInternational Journal of Pediatric Otorhinolaryngology
Volume73
Issue number10
DOIs
StatePublished - Oct 2009

Fingerprint

Kasabach-Merritt Syndrome
Hemangioma
Neck
Head
Respiratory Sounds
Platelet Count
Thrombocytopenia
Morbidity
Physicians
Biopsy
Mortality
Kaposiform Hemangioendothelioma
Neoplasms

Keywords

  • Coagulopathy
  • Hemangioendothelioma
  • Hemangioma
  • Thrombocytopenia

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Pediatrics, Perinatology, and Child Health

Cite this

Kaposiform hemangioendothelioma (with Kasabach Merritt syndrome) of the head and neck : Case report and review of the literature. / Mukerji, Shraddha S.; Osborn, Alex J.; Roberts, Jess; Valdez, Tulio A.

In: International Journal of Pediatric Otorhinolaryngology, Vol. 73, No. 10, 10.2009, p. 1474-1476.

Research output: Contribution to journalArticle

Mukerji, Shraddha S. ; Osborn, Alex J. ; Roberts, Jess ; Valdez, Tulio A. / Kaposiform hemangioendothelioma (with Kasabach Merritt syndrome) of the head and neck : Case report and review of the literature. In: International Journal of Pediatric Otorhinolaryngology. 2009 ; Vol. 73, No. 10. pp. 1474-1476.
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