Kaposiform hemangioendothelioma (with Kasabach Merritt syndrome) of the head and neck: Case report and review of the literature

Shraddha S. Mukerji, Alex J. Osborn, Jess Roberts, Tulio A. Valdez

Research output: Contribution to journalArticle

15 Citations (Scopus)

Abstract

An infant initially diagnosed with a parotid hemangioma presented with stridor and thrombocytopenia. Diagnosis of Kaposiform hemangioendiothelioma was confirmed with biopsy. The child succumbed to multi-system organ failure related to consumptive coagulopathy despite aggressive medical management. Kaposiform hemangioendiothelioma is a rare head and neck tumor that may be mistaken for a hemangioma on preliminary diagnosis, which may lead to increased morbidity and mortality especially in the setting of Kasabach-Merritt phenomenon. A platelet count may provide an early and important clue to the possibility of coagulopathy; prompting physicians to look for a diagnosis other than a simple hemangioma.

Original languageEnglish (US)
Pages (from-to)1474-1476
Number of pages3
JournalInternational Journal of Pediatric Otorhinolaryngology
Volume73
Issue number10
DOIs
StatePublished - Oct 2009

Fingerprint

Kasabach-Merritt Syndrome
Hemangioma
Neck
Head
Respiratory Sounds
Platelet Count
Thrombocytopenia
Morbidity
Physicians
Biopsy
Mortality
Kaposiform Hemangioendothelioma
Neoplasms

Keywords

  • Coagulopathy
  • Hemangioendothelioma
  • Hemangioma
  • Thrombocytopenia

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Pediatrics, Perinatology, and Child Health

Cite this

Kaposiform hemangioendothelioma (with Kasabach Merritt syndrome) of the head and neck : Case report and review of the literature. / Mukerji, Shraddha S.; Osborn, Alex J.; Roberts, Jess; Valdez, Tulio A.

In: International Journal of Pediatric Otorhinolaryngology, Vol. 73, No. 10, 10.2009, p. 1474-1476.

Research output: Contribution to journalArticle

Mukerji, Shraddha S. ; Osborn, Alex J. ; Roberts, Jess ; Valdez, Tulio A. / Kaposiform hemangioendothelioma (with Kasabach Merritt syndrome) of the head and neck : Case report and review of the literature. In: International Journal of Pediatric Otorhinolaryngology. 2009 ; Vol. 73, No. 10. pp. 1474-1476.
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