Maternal PKU

Strategies for dietary treatment and monitoring compliance

Reuben Matalon, K. Michals, L. Gleason

Research output: Contribution to journalArticle

9 Citations (Scopus)

Abstract

Blood phenylalanine and the metabolites of phenylalanine can be dramatically lowered in pregnant PKU mothers. Special formulas and a strict protocol should be used to achieve diet control and adequate compliance. Levels of blood phenylalanine of 4 mg/dl and lower can be achieved and are preferable to higher levels. The problem of treatment postconception may lead to limited success, as in our case. In order to achieve optimal results, blood phenylalanine should be controlled at or before conception. Since it is difficult to return patients to diet who have been taken off phenylalanine restriction, diet therapy for PKU should not be discontinued at any age.

Original languageEnglish (US)
Pages (from-to)223-230
Number of pages8
JournalAnnals of the New York Academy of Sciences
VolumeVol. 477
StatePublished - 1986
Externally publishedYes

Fingerprint

Maternal Phenylketonuria
Phenylalanine
Compliance
Nutrition
Monitoring
Blood
Diet
Diet Therapy
Therapeutics
Metabolites
Mothers

ASJC Scopus subject areas

  • Biochemistry, Genetics and Molecular Biology(all)

Cite this

Maternal PKU : Strategies for dietary treatment and monitoring compliance. / Matalon, Reuben; Michals, K.; Gleason, L.

In: Annals of the New York Academy of Sciences, Vol. Vol. 477, 1986, p. 223-230.

Research output: Contribution to journalArticle

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