Regional and cellular neuropathology in the palmitoyl protein thioesterase-1 null mutant mouse model of infantile neuronal ceroid lipofuscinosis

Keyphrases

• Neuropathology 100%
• Mutant Mouse Models 100%
• Null mutant Mice 100%
• PPT1 100%
• Juvenile Neuronal Ceroid Lipofuscinosis 100%
• Palmitoyl-protein Thioesterase 1 100%
• Cortical Regions 66%
• Subcortical Regions 66%
• Therapeutic Strategies 33%
• Hippocampal Neurons 33%
• Disease Pathogenesis 33%
• Lysosomal Storage Disease 33%
• Cerebellum 33%
• Neuronal Survival 33%
• Lamin 33%
• Severely Affected 33%
• Microglial Activation 33%
• Phenotypic Markers 33%
• Cortical Thinning 33%
• Interneuron 33%
• Reduced Volume 33%
• Mouse CNS 33%
• Cortical Interneurons 33%
• Astrocytosis 33%
• Disease Features 33%
• Neuronal Changes 33%

Neuroscience

• Palmitoyl Protein Thioesterase 100%
• Neuronal Ceroid Lipofuscinosis 100%
• Interneuron 100%
• Cerebellum 50%